Thalassemia Patients and Friends

Discussion Forums => The Spotlight => Topic started by: Gina Cioffi on February 14, 2006, 04:09:49 PM

Title: Congratulations on the fabulous new web site
Post by: Gina Cioffi on February 14, 2006, 04:09:49 PM
Hello,

My name is Gina Cioffi and I am privileged to serve as the National Executive Director of the Cooley's Anemia Foundation based in New York City.  If anyone needs any information or wants to learn more about our services please check out our website - www.cooleysanemia.org.  Or feel free to contact us by phone.  We recently moved offices and our new contact information is:  Cooley's Anemia Foundation, 330 Seventh Avenue, New York, NY 10001 phone 212 279-8090 or 800-522-7222. 

Lisa's family continues to raise funds through the Rochester chapter of the Foundation.  Their support for our patient and medical research programs has been tremendous and we are delighted that this support website continues to honor Lisa's contributions and interest in improving the care of patients worldwide.

Sincerely,

Gina Cioffi

Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on February 15, 2006, 03:23:22 PM
Hi Gina!  I'm so glad you joined!   :biggrin
Title: Re: Congratulations on the fabulous new web site
Post by: MicheleKH on February 15, 2006, 05:25:22 PM
Hi Gina,

Is there a way to order the red Cooley's Anemia bracelets?

Michele
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on February 17, 2006, 06:17:39 AM
Hi Michele,

I have the bracelets for sale if you'd like me to send you any.  They are $1.00 each.

If anyone else would like a rubber Thalassemia bracelet (like the Livestrong ones, only red in color), I have about 40 left, so let me know.  :biggrin
Title: Re: Congratulations on the fabulous new web site
Post by: MicheleKH on February 22, 2006, 02:08:28 PM
Hi Danielle,

I am interested in getting some for my family and friends, just tell me how to send you the money.

thanks!

Michele
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on February 26, 2006, 08:02:51 AM
Hi Danielle,
I am interested in getting some for my family and friends, just tell me how to send you the money.
thanks!
Michele

Michele, are you registered with PayPal (www.paypal.com)?  If not, would you be able to send me a check?  How many bracelets do you want?
Title: Re: Congratulations on the fabulous new web site
Post by: MicheleKH on February 27, 2006, 05:43:52 PM
Hi Danielle,

I do have a paypal account.  Let me know what I need to do.  I'd like to take 10 bracelets.

thanks,
Michele
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on February 27, 2006, 11:37:02 PM
Ok, Michele.  I'll private message you, and we'll work out the details.   :biggrin
Title: Bracelets?!
Post by: §ãJ¡Ð ساجد on March 01, 2006, 06:43:55 AM
What do these Bracelets do? I mean, are they the "Magnetic Bracelets" used by people of "Alternate Therapy"? or just a fashion accessory?

Don't know what I am talking about? Well, I will tell you another Story of the therapies in developing countries!

One day I was watching tv and while channel surfing, I found this very famous "Alternative Therapies" (Such as Meditaion, Color, Yoga, Magnet, Pressure Points :blah ) expert nicknamed "Yogi" giving an introduction to "Magnetic Thrapy". He claimed that these Magnetic braclets effects the blood flow by interacting with iron in Heamoglobin and thus curing various diseases such as muscular/joint pains, cramps etc. He also showed a Magnetic Waist belt that can cure various organs like a sick liver to make blood and stimulate the Pancrease to treat Diabetes etc.

This also reminds me of another story that there is a Homeopathic Doctor near our house. One day he told me to take some Balm (Balm is a Jelly like substance with lots of menthol and other stuff used extrenally to cure muscle cramps, headaches, cough and cold etc). Anyway, he told me to take some Balm and rub it on a particular pressure point on the liver and then message the palm of my hand (again some pressure point). He said that this will cure your liver and you won't need blood trasnfusion again!

One important point I noted that, like most people in this region they beleive that the Liver is responsible for making Blood. They don't have the slightest knowlege that it is the Stem Cells in the Bone marrow that has this job. Although this is true that if the liver malfunctions, the blood counts are also effected(Danielle you are a Med Pro, you should know better than me, what really the case is), but it is totally wrong that "Liver makes Blood!", well this is what I think! Tell me what you guys think, I'd like to hear from everyone on this one!  :jumping :wonder
Title: Re: Bracelets?!
Post by: Danielle on March 01, 2006, 07:24:49 AM
What do these Bracelets do? I mean, are they the "Magnetic Bracelets" used by people of "Alternate Therapy"? or just a fashion accessory?

Sajid, they're not the magnetic ones.  They are rubber Thalassemia bracelets, like the yellow "LiveStrong" ones they have for Cancer.  This is what they look like ...

(http://i2.photobucket.com/albums/y18/dee1207/MVC-034S.jpg)

If anyone would like to purchase them, they are $1.00 each, and all proceeds go to the Cooley's Anemia Foundation.  Just let me know.  :)
Title: Re: Bracelets?!
Post by: Danielle on March 01, 2006, 07:31:19 AM
Well, Sajid, one thing that I know for sure, is that the liver is responsible for clotting factors, and when the liver malfunctions, the clotting mechanism also malfunctions, which will eventually lead to severe bleeding.  This, in turn, will cause the blood counts to drop.  Maybe that's why they think the liver has direct responsibility for making blood, which is indeed false.   :dunno
Title: Re: Congratulations on the fabulous new web site
Post by: Andy Battaglia on March 01, 2006, 08:15:02 AM
Our infamous Dr Ghulam has also often made the claim that thal is caused by the liver and that the bone marrow has nothing to do with. But he has also told me that there has never been a successful bone marrow transplant, in spite of the fact that bmts are being done regularly and successfully in many centers around the world. The worst thing about these "healers" is they give people false hope and get them to squander their precious funds on a fraud. One more reason we need to make enlightening people about thal a daily habit.
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on March 01, 2006, 08:25:04 AM
Ok, I don't know how I'm going to explain this, but I'm going to try.  Thinking back to nursing school, there is actually a way the liver can be involved in the production of red cells.

Bare with me ...   :scared

When our bodies become hypoxic (lack of oxygen), a hormone is stimulated primarily by the kidneys in adults, called Erythropoietin.  This hormone then stimulates the marrow to produce more red cells. Some amounts of this hormone is also produced by the liver in adults.

The liver is actually the primary site of red cell production in the fetus, until the bone marrow takes over.   So, in actuality, the liver plays a small part in this in adults, but a huge part in the fetus.  So, it really doesn't have a direct responsibility for the production of cells in adulthood.

I know, it's very confusing.   :gaah
Title: Re: Congratulations on the fabulous new web site
Post by: §ãJ¡Ð ساجد on March 01, 2006, 09:08:17 AM

The liver is actually the primary site of red cell production in the fetus, until the bone marrow takes over.   So, in actuality, the liver plays a small part in this in adults, but a huge part in the fetus.  So, it really doesn't have a direct responsibility for the production of cells in adulthood.

I know, it's very confusing, but it's true.   :biggrin

But in our case the HB genes are faulty. It doesn't matter how healthy the liver is or how much Erythroprotein our kidneys make. The bone marrow will produce more of that blood with faulty HB if we take Erythroprotein shots that are available in the market. Right?!?!  :dunno :huh
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on March 01, 2006, 09:33:13 AM
Exactly, Sajid.  We will just continue to make faulty cells, no matter how much the erythropoietin is stimulating the marrow.   :sadyup
Title: Re: Congratulations on the fabulous new web site
Post by: §ãJ¡Ð ساجد on March 01, 2006, 11:09:55 AM
Our infamous Dr Ghulam has also often made the claim that thal is caused by the liver and that the bone marrow has nothing to do with. But he has also told me that there has never been a successful bone marrow transplant, in spite of the fact that bmts are being done regularly and successfully in many centers around the world. The worst thing about these "healers" is they give people false hope and get them to squander their precious funds on a fraud. One more reason we need to make enlightening people about thal a daily habit.

Hey, I know this Ghulam Haider. He is no doctor but a Hakim who uses herbal therapy. One day he added me to his MSN messenger(got my id from the old MSN forum) and started to convince me that he has the cure for thal. I didn't know about him by that time and I too thought that he was a Doctor. When I asked where his clinic was and which medicine he gives, he replied me by giving me a cell phone number and told me that his medicine is a mixture of different herbs. I asked which ones, then he said that you are not my student of Hikmat(profession of Hakim) and refused to tell me the names of the herbs. I asked him wheter he used Wheat Grass? and what benefits WG has? He said that it is not suitable for thal and it is just a markting hype of the west!

Needless to say, I just blocked him from my MSN Messenger contacts. He will no longer see me online! :naughty
Title: Re: Congratulations on the fabulous new web site
Post by: baal on March 01, 2006, 08:36:19 PM
hi dani

in this case i have to tell you something too...
a frend of mine akis (dionisos) also thal-major
30 years old...
they make a liverbiopsis at him..
and found human tissues that try to built blood cells
they called that EXTRAMEDULAERE BLUTGEWEBE
and in fact in my case...before 12 years they were
anxious about a shadow behind my pulmonic-system
and they make several CTs and later MRTs and
than they diagnostik this tissues i called you before..
i have it in my hole back..
so i thing there is a littlebit truth in the words of
the ^quacksalvers^               panos
Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on March 01, 2006, 10:26:56 PM
Hi Baal,

No one in this world knows everything that the human body is capable of, so I don't doubt what you are saying is true.  There are probably many things that the liver and other organs do that we are not aware of, and the liver may have a bigger function in the production of cells than we know.  I'm just giving factual information from what I've learned, but I definitely believe that what you are saying just may be true.  I have never heard of these particular tissues you are referring to, but this may be from a study that we do not have here in the United States.  I'm going to do some research on it.

Thanks for the info. :)
Title: Re: Congratulations on the fabulous new web site
Post by: baal on March 02, 2006, 01:38:53 AM
re dani

you are wellcome.....
look for extrmedulare bloodbuildig(dont know the english word)
the german one is extramedulaere blutbildung....
but..
in our case it doesnt helps a lot..cause ourcells are not
lifeworth...understand ?         pan
Title: Re: Congratulations on the fabulous new web site
Post by: Andy Battaglia on March 02, 2006, 01:43:43 AM
Hi Pan,

What you are saying is that more red blood cells that are useless are no help, so stimulating the liver to somehow produce more rbcs would not do any good for thals. I would go one step further and suggest that it would just be creating more useless cells for the body to dispose of through the spleen and liver causing even more problems for those organs.
Title: Re: Congratulations on the fabulous new web site
Post by: Hallu on March 02, 2006, 02:46:45 AM
Hi everybody,
This is my first post since this website is launched.  I was very tempted to jump in this conversation of RBCs production in liver.
In a recent visit to doctor, I went over the possibility of splenectomy as I have a large spleen. As per my doctor it could be risky as spleen produces some RBCs and if destruction is less than the production in spleen then splenectomy might harm as it could bring down the haemoglobin. I was quite surprised to learn that production of RBCs can happen in spleen too. I use to think spleen only deals with old/irregular RBCs clean up and immunity.
Also, the doctor told that RBCs production in just not limited to Bone Marrow, but can happen in liver, spleen and gums too. Thals frequently get swollen/big gums as a result of increased activity in gums.

Just thought to share this with you all.

Small Introduction:
I'm 31 years old, thal intermedia (HbE + Beta) located in DC metro area. My spleen is enlarged (around 20*10*8), ferritin level is 420 with saturation 36%.

I really appreciate the incredible effort made by Andy and Danielle in constructing this website which is so *impressive* and at the same time so helpful. Their contribution in the previous msn group deserves a big applause too.
I would also like to thank Faye(Id: Saugirl on thalassemiapatientsandfriends msn group) as she helped me find a haemotologist in this area.  I'm not sure whether she has joined this site or not, but if she has, I would like to let her know that i'm grateful to her.

Thanks,
Hallu.








Title: Re: Congratulations on the fabulous new web site
Post by: Danielle on March 02, 2006, 03:16:11 AM
I agree, Andy.  I guess that goes back to the reason why medications like Epogen and Procrit do not work for us.  Those medications are basically just the Erythropoietin that I was explaining about in a previous post.  If we are given Erythropoietin, it will just try to stimulate more bad cells, which is useless.
 :(

I am still going to research this tissue that Pan is talking about, because I find it very interesting.  Thanks again, Pan.   :biggrin

Hallu, nice to see you posting.  :)  I find what you say very interesting also, as I have not heard of the spleen actually producing cells, since it's part of the lymp system and actually filters the blood.  It engulfs all the old/dying red cells and breaks it down into bilirubin.  I'll have to research this as well.  Thanks.  :smileblue
Title: Re: Congratulations on the fabulous new web site
Post by: §ãJ¡Ð ساجد on March 03, 2006, 03:07:23 PM

Also, the doctor told that RBCs production in just not limited to Bone Marrow, but can happen in liver, spleen and gums too. Thals frequently get swollen/big gums as a result of increased activity in gums.


Gums!  :o :confused :noway Now this is somthing you don't hear very often! My HB remains quite low and my gums are tight as rubber. Only once I got bleeding from gums which was another story. See my post in Thal. Major section!
Title: Re: Congratulations on the fabulous new web site
Post by: Hallu on June 12, 2006, 09:28:12 PM
Hallu, nice to see you posting.  :)  I find what you say very interesting also, as I have not heard of the spleen actually producing cells, since it's part of the lymp system and actually filters the blood.  It engulfs all the old/dying red cells and breaks it down into bilirubin.  I'll have to research this as well.  Thanks.  :smileblue


Danielle/All,

I came across this piece of info and thought to share with you all :
Hypersplenism
Many patients with thalassaemia major experience
problems of the spleen - a soft, purplish organ about
the size of a fist, located on the left-hand side just
below the diaphragm, under the ribs . A normal
spleen contains 20-30ml of red blood cells. However, in
patients with persistent moderate to severe anaemia
as a result of inappropriate blood transfusion, the spleen
may hold a litre (1000ml) or more of blood. This is
because the spleen *produces extra red blood cells* in
a process known as extra med-ullary erythropoeisis - i.e.
the synthesis of red blood cells outside the normal site
of production, the bone marrow - in an effort to help
the body overcome anaemia.


--Source : http://www.thalassaemia.org.cy/books/ABOUTTHA.PDF
Page 76

--Hallu
Title: Re: Congratulations on the fabulous new web site
Post by: Kathy11 on June 13, 2006, 01:16:46 AM
Hi Hallu and all.
Thank-you for the posting of the info. about the Book written by the doctor in egypt.I'm reading it and I found it to be clear and easy to undestand.It is much appreciated.
Kind regards to everyone from kathy
Title: Re: Congratulations on the fabulous new web site
Post by: mustho on June 13, 2006, 02:18:56 AM
Hi all the extra medulary hematopoiesis is not normal condition that is one of the pathology of thalassemia, due to extramedulary hematopoiesis these frontal bossing and facial features we see in thalassemics. I think the cocept of erythropoiesis in liver and spleen is not in adults, because in fetus it happens. But in thalassemics thats becuase of demand for oxygen and hemoglobin extramedullary hematopoiesis takes place.

However the pathology of globin mutations in thalassemia leads unbalanced globin chain that further enhance early destruction of these cells. Therefore some hematologists belive its not good for thalassemics to have extramedullary hematopoiesis. Instead its always better for them to have certain level of hemoglobin constantly so that thier own erythorpoiesis will have less pathological RBC production.